Low-Grade Fibromyxoid Sarcoma: A case report from Tishreen University Hospital

Authors

  • Duaa Knaj Tishreen University
  • Michael Georgeos Tishreen University

Abstract

Background: Low-Grade Fibromyxoid Sarcoma (LGFMS) is a rare sarcoma

subtype predominantly affecting younger adults and typically presents in the

extremities and trunk. It is characterized by an indolent clinical course.

Case presentation: A-45-year woman presented with a large mass in the left lung based on chest-computed tomography (CT). A needle biopsy through chest wall from the mass and a bronchial endoscopy were done. She had a total left pneumonectomy and based on the pathology results, the tumor was

LGFMS, which was confirmed by immunohistochemistry staining and FISH study. The woman had a mass in the right thigh which was resected after a biopsy was done. This thigh mass was LGFMS. She received adjuvant chemotherapy treatment for two lines because of disease progression.

Conclusion: LGFMS is characterized by its low sensitivity to both chemo-and radiotherapy. Surgical excision with clear resection margins is the first line treatment option.

Published

2023-03-22

How to Cite

1.
كناج د, ميخائيل جرجس. Low-Grade Fibromyxoid Sarcoma: A case report from Tishreen University Hospital. Tuj-hlth [Internet]. 2023Mar.22 [cited 2024Apr.27];45(1):105-11. Available from: https://journal.tishreen.edu.sy/index.php/hlthscnc/article/view/14190